Malignant peripheral nerve sheath tumor
What is Malignant peripheral nerve sheath tumor?
This is a malignant tumor of the connective tissue surrounding nerve sheaths, usually neurofibrosarcoma or neurosarcoma. It maybe genetic as it occurs in families, especially in patients with previous neurofibromatosis. There may be painless swelling of limb, sometimes limitation of movement. Diagnosed by tumor biopsy and treated by either surgery or chemotherapy.